![](https://blogger.googleusercontent.com/img/b/R29vZ2xl/AVvXsEjo1s9cLGR_sq-LnmxF9yHWMxngkHMJgmgG1RZvpEDHVVRLImXiXentUMoYKxCkCzts7IYL2e-VpVY4nD64QpGBFjznn7Ba0JeNKkoKSb4gen6H45rrUD7rjHqQ1LWK1CJnQe-WtMmgS8U/s320/Matthew+Busch+%2523994.jpg)
When I am not riding I
enjoy watching sports - especially football being a Dolphins and Hurricanes
season ticket holder. Music is another
passion of mine but my best musical skill is listening so I enjoy going to
concerts.
![](https://blogger.googleusercontent.com/img/b/R29vZ2xl/AVvXsEgt3G945fgCMWyIRBNG5lwLOVAV2oJ0V0sv0QIQcH8ohhlNlL9oZmECZfkgPWMi5GW4d_jl9Zt-JysEvK3-smDQc4we-Za3umVuPPTV-GkIVMRsj09C3F3U5SUa5scRnCE9hTUQErjDXe4/s320/Matthew+Busch+%2523994+C.jpg)
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I have ridden over 1K
miles in a day many times but never over this length of time. Most of my riding
trips have been 300 to 500 miles per day touring over multiple weeks with one
or two long days to stage the next part of the ride. I believe it will be one of the most physically
and mentally demanding challenges I have faced. I look forward to accepting the
challenge and pushing myself to a new level of riding.
But most of all I look
forward to meeting riders like myself that enjoy riding distances and seeing
the country the best way – on two wheels! The best advice I have
been given so far is to be ready for anything and don’t bring anything you
don’t plan to use.
![](https://blogger.googleusercontent.com/img/b/R29vZ2xl/AVvXsEh4g62jWFXkmaD_I7vT2OZDuJ9xDyVO5x7UrGzN0OZMJXfMf8Xv_JDc1J_gvgdjjAEjaqebghmTvqKGfe5h4uJG76k6nX7fEc5r0GxZREAl5BpX5Hfh2MPx9zHTAMD_YtYKbKMAnP9JoDU/s320/Matthew+Busch+%2523+994+B.jpg)
I am supporting the MPS
SuperHero Foundation. The MPS SuperHero Foundation Is a
South Florida parent-led 501(c)(3) nonprofit organization established in
2016 that is searching for a treatment solution for MPS(Mucopolysaccharidosis) II or Hunter Syndrome.
MPS II, is a progressively degenerative genetic
disease that almost exclusively affects males. Boys with MPS II are deficient
in the enzyme iduronate-2-sulfatase that helps breakdown glycosaminoglycans
(GAG). The net result is that GAG builds up in cells and organs throughout the
body. Because this chemical decomposition is unable to happen, these cells
continuously accumulate to toxic levels and build up can lead to a fairly
uniform plethora of symptoms and can begin around 2-5 years of age. These
symptoms include stunted growth, coarse facial features, stiff joints,
intellectual disability, serious physical deformities, significant damage to
the brain & organ function and eventually leads to premature death. The
severe form often includes progressive cognitive impairment and a life span of
approximately 12-15 years old. Currently, there is no cure for individuals
affected by this disease, which is why funding to bring the research by geneticists
to the first phase of human clinical trials is so crucial.
I have a family friend
that has a son with MPS II. This is a horrible disease and we are hopeful for a
cure.
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